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KMID : 0882420070730001095
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Korean Journal of Medicine
2007 Volume.73 No. 0 p.1095 ~ p.1100
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Swyer-James syndrome mimicking pulmonary thromboembolism in a patient with microscopic polyangiitis
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Park Jee-Na
Na Seung-Yeon
Lee Yeon-Ah
Lee Sang-Hoon
Hong Seung-Jae
Yang Hyung-In
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Abstract
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A 66-year-old man was admitted to our institution with a one-month history of benumbed extremities and a small amount of hemoptysis. Laboratory findings showed microscopic hematuria and proteinuria along with a positive P-ANCA test. The third day after admission, he developed dry gangrene and motor weakness in the upper and lower extremities. Nerve biopsy demonstrated leukocytoclastic vasculitis. Microscopic polyangiitis was diagnosed based on clinical and pathological clues. Despite sufficient oxygen therapy, his respiratory status suddenly deteriorated, and the possibility of pulmonary thromboembolism was suggested. Pulmonary perfusion scintigraphy showed markedly decreased perfusion in the right lung. However, chest CT revealed hypoplasia of the left pulmonary artery and hyperlucency on the left lung, which are consistent with Swyer-James syndrome, a non-filling defect in the pulmonary arteries. There has been no report of a case of Swyer-James syndrome accompanied by MPA. We here report a case of Swyer-James syndrome mimicking pulmonary thromboembolism in a patient with microscopic polyangiitis.(Korean J Med 73:S1095-S1100, 2007)
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KEYWORD
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Microscopic polyangiitis, Swyer-James syndrome
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